Glucose concentrations ranged 1. 641 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The aims of this case report are to highlight metabolic encephalopathy as a complication of DKA and to explore the. Hypoglycaemia is a BGL low enough to cause signs and/or symptoms of impaired brain function and neurogenic response - generally BGL <3. Hyperplasia of pancreatic islet beta cells NOS. E11. 64 Type 2 diabetes mellitus with. Given these severe consequences, the prompt diagnosis and. Metabolic encephalopathy is a rare but potentially devastating complication of diabetic ketoacidosis (DKA). Respiratory chain defects can also lead to hypoglycaemia during the. Hypoglycemia (Low Blood Glucose) Throughout the day, depending on multiple factors, blood glucose (also called blood sugar) levels will vary—up or down. All neoplasms, whether functionally active or not. ICD-10-CM Diagnosis Code E10. The most common causes are diabetes mellitus and idiopathic ketotic hypoglycaemia (IKH) but a number of endocrine disorders and inborn errors of metabolism (IEMs) need. The 2024 edition of ICD-10-CM E16. In. 637. E13. 01. Context: Childhood ketotic hypoglycemia (KH) is a disease characterized by fasting hypoglycemia and increased levels of ketone bodies. ICD-10 Look Up. Hypoglycemia is often defined by a plasma glucose concentration below 70 mg/dL; however, signs and symptoms may not occur until plasma glucose concentrations drop below 55 mg/dL. 64X E11. E11. 65 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. A few miscellaneous. [4] [5] Symptoms include signs of dehydration, weakness, leg cramps, vision problems, and an altered level of. E09. HHNS can affect both types of diabetics, yet it usually occurs amongst. Mol Genet Metab. 4% of all significant hypoglycemic. This is normal. Hypoglycemia Nursing Care Plan 1. ICD-9-CM 251. There is a 3-6-liter fluid deficit in DKA and almost 8 to 10 Liters in HHS. Idiopathic ketotic hypoglycemia (IKH) is an important cause of emergent hypoglycemia among children. Case report 1. e. Desired Outcome: The patient must have a blood. It is found in the 2024 version of the ICD-10 Clinical Modification (CM) and can be used in all HIPAA-covered transactions from Oct 01, 2023 - Sep 30, 2024. Type 1 dm with moderate nonproliferative diabetic retinopathy without macular edema, left eye (e10. The ICD code E160 is used to code Hypoglycemia. Type 2 diab w hyprosm w/o nonket hyprgly-hypros coma (NKHHC); Diabetes type 2 with hyperosmolarity; Hyperosmolarity without nonketotic hyperglycemic hyperosmolar coma due to type 2 diabetes mellitus. 1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. ICD-9-CM 251. In systemic carnitine deficiency, an early phase of nonketotic hypoglycemia and liver dysfunction may precede a late phase of encephalopathy and myopathy. 2 Definitions Manual:. In most medical contexts, the term diabetic coma refers to the diagnostical dilemma. The cause of of ketotic hypoglycemia, the commonest form of hypoglycemia in childhood, is not known. 01. 00 ICD-10 code E08. H40. Volume resuscitation: fluid deficit often 6-10 liters. Idiopathic ketotic hypoglycemia (IKH) is an important cause of emergent hypoglycemia among children. , . Hypoketotic hypoglycemia affects your blood sugar (glucose) level and energy. If you have any questions or concerns, please speak to the metabolic team. 00 for Diabetes mellitus due to underlying condition with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) is a medical classification as. E15 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Diabetic ketoacidosis (DKA), hyperglycemic hyperosmolar state (HHS), lactic acidosis (LA), and hypoglycemia are acute and potentially life-threatening complications of diabetes. 51 - other international versions of ICD-10 E72. All ketotic hypoglycemic children developed symptomatic hypoglycemia (33±3 mg/100 ml) and ketosis (β-OHB, 3. In neonates <48 hrs old, there is a lack of consensus on what constitutes normal BGL, however, BGL <2. This case highlights the dramatic cognitive decline of a young man due to metabolic encephalopathy complicating DKA. Urinating often. Other related topics include:Severe, non-fasting and non-ketotic hypoglycaemia should always be identified and investigated further. Functional hyperinsulinism. 11 Drug or chemical induced diabetes mellitus with ketoacidosis with coma. Medium chain acyl-CoA dehydrogenase. Source ICD-10-CM Code Target ICD-9-CM Code; E11. Short description: Diabetes due to underlying condition w hypoglycemia w/o coma The 2024 edition of ICD-10-CM E08. The 2024 edition of ICD-10-CM E11. E0800: Diabetes mellitus due to underlying condition with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) E0801: Diabetes mellitus due to underlying condition with hyperosmolarity with coma. E16. After the bolus is administered, an IV infusion that matches normal hepatic glucose production (approximately 5-8 mg/kg/min in an infant and about 3-5 mg/kg/min in. 10/10/2019. 1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. In neonates <48 hrs old, there is a lack of consensus on what constitutes normal BGL, however, BGL <2. DWI: often no anomaly 6-9. D50-D53 Nutritional anemias. 2 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. 9 became effective on October 1, 2023. 00: Type 2 diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) E11. 51 is a billable diagnosis code used to specify non-ketotic hyperglycinemia. DRG 638. Hyperosmolar hyperglycemic state (HHS) (previously known as hyperosmolar non-ketotic coma (HONK)) is a serious metabolic derangement that can occur in patients with diabetes mellitus , predominantly those with type 2. Billable Thru Sept 30/2015. Sugar is the best treatment. Metabolic encephalopathy is a rare but potentially devastating complication of diabetic ketoacidosis (DKA). 649 Type 1 diabetes mellitus with hypoglycemia without coma;. Respiratory chain defects. There are no large studiesHypoglycemia is the result of defects/impairment in glucose homeostasis. ICD-9-CM 251. 1111/j. E13. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM. Gangrene* E10. 2017 Icd 10 Cm Diagnosis Code P70. Short description: Oth diabetes mellitus with hyperosmolarity with coma The 2024 edition of ICD-10-CM E13. ICD-10-CM Code. 0 Definitions Manual. Having stomach pain. Some people develop symptoms at slightly higher levels, especially when blood. Acute treatment of adrenal crisis is for rapid restoration of tissue perfusion. E11 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail. 65 [convert to ICD-9-CM] Hypoglycemia in patients with diabetes: generally described as ≤ 70 mg/dL (≤ 3. The incidence of hypoglycemia is lower in t2dm than in t1dm. This is the American ICD-10-CM version of E11. The 2024 edition of ICD-10-CM E11 became effective on October 1, 2023. Desired Outcome: The patient must have a blood. Despite hypoglycemia is one of the most common emergencies in neonatal age and childhood, no consensus on the definition and diagnostic work-up exists yet. When glucose levels are 200 mg/dL, a fluid containing 5%-10% dextrose should be used to allow insulin to be continued until ketonemia has been corrected without causing hypoglycemia. Introduction Idiopathic ketotic hypoglycemia (KH) is the most common cause of hypoglycemia in non-diabetic children ages 0. Endocrine, nutritional and metabolic diseases. 2003 Jul;25 (1):39-43. This is the American ICD-10-CM version of E11. Respiratory chain defects. 51 is a billable diagnosis code used to specify non-ketotic hyperglycinemia. If the changes are unilateral, then they are contralateral to the symptomatic side 2 . You may browse the classification by using the hierarchy on the left or by using the search functionality. 65 may differ. 1 should only be used for claims with a date of service on or before September 30, 2015. 1 should only be used for claims with a date of service on or before September 30, 2015. 2x Secondary diabetes mellitus with hyperosmolarity;. Conditions to consider in the differential diagnosis of hypoglycemia include the following: Adrenal insufficiency - Primary adrenal disease (Addison disease); ACTH deficiency. For example, the renal complications in E10. 251. Ganister disease J62. [ 13, 14] Two patients presented with focal motor seizures, two with myoclonic jerks, and one with generalized tonic-clonic seizures. 1 Introduction. e. This condition presents with a clinical syndrome consisting of profound hyperglycemia, hyperosmolality, and dehydration. ICD 10 AM Edition: Tenth edition Query Number: 3026 34/40 pregnant lady with pre-existing type 1 diabetes admitted with 2 week history of nausea and vomiting and unstable blood sugars. 10. Despite hypoglycemia is one of the. 5–6 years old and typically occurs after a period of poor food intake. Ketotic Hypoglycemia (Fasting/Starvation) – most common cause Transient Neonatal Hypoglycemia Hyperinsulinism (transient and. You can also check out ICD-10 Codes for Diabetes Mellitus Type 1. Type 1 Excludes. 01: Type 2 diabetes mellitus with. Instead of placing my primary focus on including carbohydrates with each meal and snack, I began to focus on eating. Hypoglycemia continues to be an important cause of morbidity in neonates and children. This is the American ICD-10-CM version of E10. E11. E10. 00 may differ. Short description: OTH SPCF HYPOGLYCEMIA. Disorder of glucose metabolism 126877002. 00. D50-D89. 00 Type 2 diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC). ICD-10-CM Coding Rules. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes). 3 mmol/L. 39 Diabetes mellitus due to underlying condition with other diabetic. , diagnostic plasma glucose threshold, definition of at–risk neonates) of childhood hypoglycemia. from the Pediatric Endocrine Society for Evaluation and Management of Persistent Hypoglycemia in Neonates, Infants, and Children. During the neonatal and infant periods, hyperinsulinemic hypoglycemia (HH) is the most common etiology of refractory hypoglycemia resulting from congenital gene mutations. 69 - other international versions of ICD-10 E10. 39 - other international versions of ICD-10 Z86. 9 may differ. Ketotic Hypoglycemia Diagnosis | : Ich Tue Mein Bestes Ich Und Du Bilder Ich Will Einen Mann Der Weiß Was Er Will Ich War Noch Niemals In New York Deutsches Theater Validity Of Icd 10 Cm Codes For Determination Of Diabetes Type For Persons With Youth Onset Type 1 And Type 2 Diabetes Bmj Open Diabetes. Ketotic Hypoglycemia Icd 10 . 1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. Ketotic hypoglycemia 20825002. 649 in processing claims, check the. Hyperglycemic hyperosmolar non-ketotic (HHNK) syndrome is thought to be a rare entity in the pediatric population, associated with significant mortality based on case reports in the literature. MDC 10 Endocrine, Nutritional & Metabolic Diseases & Disorders. or very low (hypoglycemia). It is found in the 2024 version of the ICD-10 Clinical Modification (CM) and can be used in all HIPAA-covered transactions from Oct 01, 2023 - Sep 30, 2024 . Insulinoma is a type of functional neuroendocrine tumor (NET) that manifests with hypoglycemia caused by inappropriately high insulin secretion. Towards enhanced understanding of idiopathic ketotic hypoglycemia: A literature review and introduction of the patient organization, Ketotic Hypoglycemia International. 5 mL/kg. 2-2. 8 is a billable diagnosis code used to specify type 2 diabetes mellitus with unspecified complications. 83] [ICD-10 Codes: G31. Methods: Retrospective review of all medical records with a primary or secondary diagnosis of hypoglycemia (ICD-9 code 251. The 2024 edition of ICD-10-CM E13. E10. 31 Most children outgrow this condition by 5-6 years of age. However, the presence of ketones. Source: 2. without nonketotic hyperglycemic-hyperosmolar coma (NKHHC). There is a classical form of NKH and a variant form of NKH. Severe hypoglycemia: Dizziness, fatigue, weakness, headaches, inability to concentrate, confusion, slurred speech, blurred vision, seizures, and coma. Unstable Blood Glucose Level. Hypoglycemia, also known as low blood sugar or low blood glucose, is when blood sugar decreases to below normal levels. While there are no distinct imaging features, it is useful for a radiologist. ICD 10 codes in the ICD-10-CM and ICD-10-PCS replace and update all three. 65: Type 1 diabetes mellitus with hyperglycemia: E10. The charts of 94 non-diabetic patients presenting to an ED during a period of 64 months with a diagnosis of hypoglycemia as identified via ICD-9 codes were reviewed. Results: Thirty-one patients were identified. 3. 0 may differ. 52 ICD-10-CM Guideline: Causal relationship presumed with diabetes unless documentation states unrelated. Functional nonhyperinsulinemic hypoglycemia. 21 if the kidney problem is diabetic nephropathy,. 1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. Originally described by Colle and Ulstrom in 1964, IKH is defined by periodic episodes of hypoglycemia, associated with ketonuria, in an. [1] Chorea is considered a special complication and is very rare; the overall clinical features of the disease remain unknown. 3 - other international versions of ICD-10 Y92. The symptoms of Whipple's triad have been used to describe hypoglycemia since 1938. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or. ICD-10-CM Code for Diabetes mellitus due to underlying condition with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) E08. 69 - other international versions of ICD-10 E11. 9 became effective on October 1, 2023. 8 is a billable diagnosis code used to specify type 2 diabetes mellitus with unspecified complications. Showing 1-25: ICD-10-CM Diagnosis Code E16. The classical form is then further divided into severe. Eleven patients, accounting for 24. This is the American ICD-10-CM version of E11 - other international versions of ICD-10 E11 may differ. It is commonly seen in elderly women. E11. 2005. For episodes of preoperative fasting or febrile illness, intravenous glucose (10% dextrose. This is the American ICD-10-CM version of E11. T1 : hyperintense. 3, 4 Idiopathic KH can be. Glycine also acts as a neurotransmitter, which is a chemical messenger that transmits signals in the brain. E11. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism. 65 became effective on October 1, 2023. Typically the children were `dysmature' at birth, with a history suggesting hypoglycaemia in the first 36 hours of life, and they have remained small and thin. Hypoglycemia in patients without diabetes < 55 mg/dL symptoms of hypoglycemia [3] Whipple triad [4] [5] Low blood glucose levels. Abstract. Severe hypokalemia and severe hypoglycemia are associated with higher hospital mortality in patients with hyperglycemic crises. This case highlights the dramatic cognitive decline of a young man due to metabolic encephalopathy complicating DKA. Hypoglycemic disorder 237630007. blogspot. This is the American ICD-10-CM version of Y92. 618 [convert to ICD-9-CM] Type 2 diabetes mellitus with other diabetic arthropathy. 1, 2 A larger part of KH patients have idiopathic KH, a diagnosis of exclusion believed to represent a genetic and clinical heterogeneous disease entity. 900-0164-0218 Updated February 2018Objective To investigate nonketotic hyperglycemia (NKH)-related epileptic clinical features and pathogenesis, and improve the diagnosis and treatment. 00 contain annotation back-references ICD 10 code for Type 2 diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC). This is the American ICD-10-CM version of E11. Citation, DOI, disclosures and article data. This is the American ICD-10-CM version of E13. Drug-induced hypoglycemia without coma. 65. 2 should only be used for claims with a date of service on or before September 30, 2015. Hyperglycemia, unspecified. Initial signs and symptoms of this disorder typically occur during infancy or early childhood and can include poor appetite. In a retrospective review comparing 8550 adult patients with diabetic ketoacidosis admitted to an intensive care unit where blood glucose was corrected to 10 mmol/L (180 mg/dL) or lower or to above 10 mmol/L (180 mg/dL) within 24 hours, those in the latter group had less hypoglycemia, hypokalemia, and hypo-osmolality, with lower. It is found in the 2022 version of the ICD-10 Clinical Modification (CM) and can be used in all HIPAA-covered transactions from Oct 01, 2021 - Sep 30, 2022 . 84]. This is the American ICD-10-CM version of E72. INTRODUCTION. In individuals without diabetes, hypoglycemia is a clinical syndrome with diverse causes. The administration of biotin 10 mg/day provides a dramatic and sustained improvement. Patients often have a recent bout of heavy drinking before the period of relative. 10. Hypoglycemia / Recurrent Hypoglycemia [ICD-9 Code: 251. 4%. It is found in the 2022 version of the ICD-10 Clinical Modification (CM) and can be used in all HIPAA-covered transactions from Oct 01, 2021 - Sep 30, 2022 . , dextromethorphan, oral ketamine) to reduce glycinergic stimulation. There are several forms of the disease,. . Before loss of consciousness and coma takes place, patients will display signs of very high blood sugar levels which may include: Extreme thirst. Next Code: E11. A type 1 excludes note is a pure excludes. pathic ketotic hypoglycemia” and “ketotic hypoglycemia” yielded neither an Orpha number, an Online Mendelian Inheritance in Man (OMIM) geno- or phenotype refer-ence number, or an ICD-10 number. （英語：Hypoglycemia、low blood sugar）是指 中——特別是 中——的葡萄糖浓度（ ）低于正常水平的现象，一般是治疗 时的并发症，也可能是由多种原因所引起的，并导致一系列临床的综合 低血糖症Hypoglycemia [1] [2] [3] 低血糖可能會導致. The 2024 edition of ICD-10-CM H40. The coding system was updated in October 2015 to its 10th revision because it was thought that the 9th revision (ICD-9) no longer. 65 - other international versions of ICD-10 E10. Normoglycemic ketonemia is a common biochemical presentation in patients with GSD types VI and IX, and ketonemia can precede hypoglycemia in all studied GSD types. It means "not coded here". 00 Drug or chemical induced diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) ICD-10-CM: E09. E72. 9 - other international versions of ICD-10 H40. ICD-9-CM 251. BILLABLE | ICD-10 from 2011 - 2016. Search Results. 65 may differ. E72. Mol. E13. Objectives To examine the clinical presentations and. Disorders in glucose availability or utilization can result in hypoglycemia or hyperglycemia. Pediatr Rev (1989) 11 (4): 117–124. 65 may differ. Medium chain acyl-CoA dehydrogenase. The brain’s two most critical sources of energy are sugar. Replete with 1L/hr x 2-4 hours to start. Ketotic hypoglycemia. ICD-9-CM 251. Ganser's syndrome F44. 69 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Ketotic hypoglycemia. 65 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Nausea and vomiting caused by ketones may lead to further decline in PG if hyperketosis is not recognized and treated. Includes. DRG 638 DIABETES WITH CC. In the United States, the. 0 - other international versions of ICD-10 E16. It is found in the 2024 version of the ICD-10 Clinical Modification (CM) and can be used in all HIPAA-covered transactions from Oct 01, 2023 - Sep 30, 2024 . A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition. Gastralgia - see also Pain, abdominal. Division of Emergency Medicine, Children's Hospital of Philadelphia, 34th Street and Civic Center Boulevard, Philadelphia, PA 19104, USA. 1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. Symptoms of HONK. Metabolic disease 75934005. The exact specificities are not clear, as there does not seem to be obvious defects in metabolism but it is important to rule out other causes of hypoglycemia that can also produce ketosis. ICD-9-CM 251. Abstract. Next Code: E88. 51 is a valid billable ICD-10 diagnosis code for Non-ketotic hyperglycinemia . ICD-10-CM Diagnosis Code T38. 0 - other international versions of ICD-10 E11. 00 became effective on October 1, 2023. 00 for Type 2 diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) is a medical classification as listed by WHO under the. This is the American ICD-10-CM version of Z86. 01 became effective on October 1, 2023. E08: Diabetes due to underlying condition. Hypoglycemia is a clinical situation characterized by a reduction in plasma glucose concentration to a level that may induce symptoms or signs such as altered mental status and/or sympathetic nervous system stimulation. Other related topics include:4 for hypoglycemia ; 5 for hyperglycemia ; 6 for other complications. 1 should only be used for claims with a date of service on or before September 30, 2015. 8. 3-hydroxyacyl-CoA dehydrogenase deficiency is an inherited condition that prevents the body from converting certain fats to energy, particularly during prolonged periods without food (fasting). 9 mmol/L; betahydroxybutyrate was up to 5. ICD-9 and 10 codes for definition of diabetes and cirrhosis-related complications (ascites and hepatic encephalopathy). doi: 10. Mutations in the GLDC or AMT gene cause nonketotic hyperglycinemia. Hyperglycemic hyperosmolar non-ketotic (HHNK) syndrome is thought to be a rare entity in the pediatric population, associated with significant mortality based on case reports in the literature. pathic ketotic hypoglycemia” and “ketotic hypoglycemia” yielded neither an Orpha number, an Online Mendelian Inheritance in Man (OMIM) geno- or phenotype refer-ence number, or an ICD-10 number. Hypoketotic hypoglycemia, cardiomyopathy, liver disease, recurrent rhabdomyolysis Medium-chain Acyl-CoA dehydrogenase deficiency Reye-like syndrome, metabolic crisis after fasting with lethargy. Hyperglycemia-induced seizures are refractory to antiepileptic medications, account for 15–40% of seizures in patients with HHS, and are commonly focal motor seizures and epilepsia partialis continua. 10. 1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 251. 9 in processing claims, check the following: — See. Find out more. 00 ICD-10 code E11. Nonketotic Hyperglycinemia (NKH) is a genetic disorder characterized by abnormally high levels of glycine, an amino acid that is one of the “building blocks” of proteins. Short description: OTH SPCF HYPOGLYCEMIA. 5. Patients often have a recent bout of heavy drinking before the period of relative. The cause is unknown. Ketotic hypoglycemia (KH) is not a disease itself. MRI of the brain is the modality of choice for assessing possible non-ketotic hyperglycaemic hemichorea and typically demonstrates signal changes, particularly in the putamen and/or caudate 1-3. There are no large studies looking at the value of common laboratory testing in children presenting with KH or how often other diagnoses are made. springernature. įind, Read, And Discover Icd 10. 11 Drug or chemical induced diabetes mellitus with ketoacidosis with coma. ICD-10-CM Guideline: Use additional code to identify site and severity of ulcer. Clinical finding 404684003. Type 1 diabetes mellitus with hypoglycemia without coma. Impairments in counterregulatory responses and hypoglycemia. Objective: The objective of the study was to study a pair of homozygotic twin boys, one of whom had severe KH from the age of 14 months, whereas the other boy was. Hyperosmolar hyperglycemic state ( HHS ), also known as hyperosmolar non-ketotic state ( HONK ), is a complication of diabetes mellitus in which high blood sugar results in high osmolarity without significant ketoacidosis. 51. 641 in processing claims, check the. 70±0. The 2024 edition of ICD-10-CM E11. Hypoglycemia Nursing Care Plan 1. ICD-9-CM 251. 00 - other international versions of ICD-10 E13. The 2024 edition of ICD-10-CM E10. Hypoglycaemic attacks started at the age of 3 years and 4 months and continued until 9. 4 Other Neonatal Hypoglycemia. 12. Thus, treatment focuses on reducing plasma glycine concentration by initiating sodium benzoate therapy and utilizing N-methyl-D-aspartate receptor site antagonists (i. For Whipple's triad, the practitioner must first recognize. The mission of KHI is to enhance the understanding of IKH for the benefit of children, parents, and families who have been affected by IKH. A search of Orphanet for “idiopathic ketotic hypoglycemia” and “ketotic hypoglycemia” yielded neither an Orpha number, an Online Mendelian Inheritance in Man (OMIM) geno- or phenotype reference number, or an ICD-10 number. 9, to enhance healthcare accuracy and patient outcomes. Hypoglycemia; Hypoglycemia (low blood sugar); Hypoglycemia post gi surgery; Hypoglycemia unawareness; Hypoglycemic encephalopathy; Loss of hypoglycemic warning; Post gastrointestinal tract surgery. The 2024 edition of ICD-10-CM E11. 69. Nursing Diagnosis: Unstable Blood Glucose Level related to insufficient checking of blood sugar levels and lack of compliance to proper diabetes management secondary to hypoglycemia as evidenced by fatigue and tremors. If both parents are heterozygous.